The congenital cystic dilatation of biliary ductal system due to a developmental defect is not common disease´ entity. It usually-lead to bile stasis, predisposes to bacterial growth, compression of parenchyma) cells and associated impairment of -liver function.
Although hundreds cases of the cystic dilatation of the extrahepatic duct have been reported the congenital cystic dilatation´of the intrahepatic duct has been in lower incidence, less than about 20 cases so far.
The cystic dilatation of the extrahepatic duct is usually diagnosed by classic symptom triad, and cholangiogram. And the upper G-I series and intravenous pyelogram are quite helpful.
The diagnosis of the cystic dilatation of the intrahepatic duct, however, are rather difficult, which is usually detected by operative cholangiogram and/or percutaneous transhepatic cholangiogram.
The surgical intervention is only treatment, such as excision, internal drainage and sometimes hepatic resection.
We have experienced one patient with choledochal cyst and two with congenital cystic dilatation of intrahepatic duct, the postoperative course was uneventful.
|